Congenital Heart Disease and Pregnancy

Pulmonary hypertension of any cause is associated with a 50% maternal mortality. Other high-risk cardiac conditions are severe mitral, pulmonary or aortic stenosis and Marfan's syndrome with a dilated aortic root. Intracardiac shunts without pulmonary hypertension are relatively safe but require closer follow-up. Operated tetralogy of Fallot without residual pulmonary stenosis is lower risk; coarctation is associated with dissection and is intermediate risk.